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La Balma en el siglo XX: El puente sobre el Bergantes

In document Historia de Nuestra Señora de la Balma (página 131-138)

regurgitation.  

• Collapsing  pulse.  

• Early  diastolic  murmur.  

• Wide  pulse  pressure  (need  reading  with  heart  beat).    

• Dancing  uvula.  

• Dancing  capillaries  with  beat.    

Fasciculation     • Normal  when  stick  out  tongue.  

• To  find  pathology,  leave  tongue  in  mouth.  

• LMN  –  Motor  neuron  disease  –  Fasciculation  everywhere.    

 

3. Face  and  others    

Endocrine     Grave’s,  acromegaly,  Cushing’s.    

CVS     Sternotomy   (CABG),   hyperlipidemia   (arcus   lipidus),   central   cyanosis,   clubbing,   congenital   cyanotic   heart   diseases,   Eisenmenger  syndrome.    

Neurology     • Bell’s   palsy   :   Absence   of   forehead   wrinkles,   nasolabial   fold   (7th).    

• Ptosis,  eyeball  down  and  out  (3rd).  

Nephrology     • CRF  –  Sallow  face  (lighter  than  tea  colour),  uremic  breath.  

• Nephrotic  syndrome  –  Peri-­‐orbital  edema.    

Hepatology   Alcoholic   cirrhosis   –   Ascites,   gynecomastia,   female   public   hair   distribution.    

Rheumatology   • SLE  –  Butterfly  rash.    

• RA  +  Swan  neck  deformity  +  Dry  eyes  and  mouth  =  Sjogren’s   syndrome.  

• Dermatomyositis  –  Heliotrope  rash.    

 

4. Hands  and  others    

Hands   • Acromegaly  (spade  like).  

 

• Darkening  of  palmar  creases    (+  pigmentation  in  mouth)  –  ACTH,   Addison’s  disease.  Unable  to  produce  cortisol,  so  feedback  is  to   increase   the   production   of   ACTH   (same   structure   as   MSH),   leading  to  hyperpigmentation.    

 

• Raynaud’s  phenomenon  :  White  à  Blue  à  Pink     -­‐ The  symptoms  include  several  cyclic  color  changes  

1. When  exposed  to  cold  temperatures,  the  blood  supply  to  the   fingers   or   toes,   and   in   some   cases   the   nose   or   earlobes,   is   markedly  reduced;  the  skin  turns  pale  or  white  (called  pallor),   and  becomes  cold  and  numb.  

2. When   the   oxygen   supply   is   depleted,   the   skin   colour   turns   blue  (called  cyanosis).    

3. These  events  are  episodic,  and  when  the  episode  subsides  or   the   area   is   warmed,   the   blood   flow   returns   and   the   skin   colour  first  turns  red  (rubor),  and  then  back  to  normal,  often   accompanied   by   swelling,   tingling,   and   a   painful   "pins   and   needles"  sensation.  

 

-­‐ In   men,   this   phenomenon   sometimes   occurs   in   individuals   who  work  with  vibrating  instruments.  

-­‐ In   patients   with   systemic   scleroderma,   attacks   are,   in   general,  more  frequent  and  more  severe.    

 

• Cervical  spondylitis.  

• Osler’s  nodes  (painful),  Janeway  lesions  (painless).    

• Ulnar  claw  –  4th  and  5th  fingers  drawn  towards  the  back  of  the   hand   at   the   first   knuckle   and   curled   towards   the   palm   at   the   second  and  third  knuckles.  

 

   

• Dupuytren’s   contracture   in   CRF   –   Fixed   flexion   contracture   of   the  hand  where  the  fingers  bend  towards  the  palm  and  cannot   be   fully   extended   (straightened).   Due   to   contractures   of   the   palmar  aponeurosis  (or  palmar  fascia).  

 

   

• Mixed  CT  disease  ("Sharp's  syndrome")     -­‐ Autoimmune  disease.    

-­‐ Combines   features   of   scleroderma,   myositis,   SLE,   and   RA   (with   some   sources   adding   polymyositis,   dermatomyositis,   and   inclusion   body   myositis),   and   is   thus   considered   an   overlap  syndrome.  

-­‐ Commonly   causes   joint   pain/swelling,   malaise,   Raynaud’s   phenomenon,   Sjögren's   syndrome,   muscle   inflammation,   sclerodactyly   (thickening   of   the   skin   of   the   pads   of   the   fingers).    

-­‐ Lichenification   –   Thick,   leathery   skin,   usually   the   result   of   constant  scratching  and  rubbing.  

         

 

   

• Livedo  reticularis  

-­‐ Mottled  reticulated  vascular  pattern  that  appears  like  a  lace-­‐

like   purplish   discoloration   of   the   lower   extremities.   The   discoloration  is  caused  by  swelling  of  the  medium  veins  (not   small)  in  the  skin,  which  makes  them  more  visible.  So  it  can   be  caused  by  any  condition  that  makes  venules  swell.  

-­‐ Broad   differential   diagnosis,   broadly   divided   into   possible   blood   diseases,   autoimmune   (rheumatologic)   diseases,   cardiovascular   diseases,   cancers,   and   endocrine   disorders.  

SLE,  anti-­‐phospholipid  syndrome,  Sneddon's  syndrome.  

 

     

• Boutonniere  deformity  (“Button  through  button  hole”)  

-­‐ Deformed  position  of  the  fingers  or  toes,  in  which  the  joint   nearest   the   knuckle   (PIP)   is   permanently   bent   toward   the   palm   while   the   furthest   joint   (DIP)   is   bent   back   away   (PIP   hyperflexion   with   DIP   hyperextension).   It   is   commonly   caused  by  injury  or  by  an  inflammatory  condition  like  RA.    

-­‐ This  flexion  deformity  of  the  proximal  interphalangeal  joint  is   due  to  interruption  of  the  central  slip  of  the  extensor  tendon   such   that   the   lateral   slips   separate   and   the   head   of   the   proximal  phalanx  pops  through  the  gap  like  a  finger  through   a   button   hole   (thus   the   name,   from   French   boutonnière  

"button   hole").   The   distal   joint   is   subsequently   drawn   into   hyperextension   because   the   two   peripheral   slips   of   the   extensor   tendon   are   stretched   by   the   head   of   the   proximal   phalanx  (note  that  the  two  peripheral  slips  are  inserted  into   the  distal  phalanx,  while  the  proximal  slip  is  inserted  into  the   middle   phalanx).   This   deformity   makes   it   difficult   or   impossible  to  extend  the  proximal  interphalangeal  joint.  

 

   

• Scleroderma,  psoriasis,  vasculitis.  

 

• Tophaceous   gout   –   A   chronic   form   of   gout.   Nodular   masses   of   uric   acid   crystals   (tophi)   are   deposited   in   different   soft   tissue  

areas  of  the  body.  Even  though  tophi  are  most  commonly  found   as   hard   nodules   around   the   fingers,   at   the   tips   of   the   elbows,   and  around  the  big  toe,  tophi  nodules  can  appear  anywhere  in   the  body  (e.g.  ears,  vocal  chords,  spinal  cord).      

 

• Digital  gangrene   -­‐ Atherosclerosis.  

-­‐ Vasculitis.  

-­‐ IgA   nephropathy   (Berger's)   –   Primary   IgA   nephropathy   is   characterized   by   deposition   of   the   IgA   antibody   in   the   glomerulus.   There   are   other   diseases   associated   with   glomerular   IgA   deposits,   the   most   common   being   Henoch-­‐

Schönlein  purpura  (HSP),  which  is  considered  by  many  to  be   a   systemic   form   of   IgA   nephropathy.   HSP   presents   with   a   characteristic   purpuric   skin   rash,   arthritis,   and   abdominal   pain  and  occurs  more  commonly  in  young  adults.    

 

• Marfan’s  

-­‐ Arachnodactyly   (fingers   are   abnormally   long   and   slender   in   comparison  to  the  palm  of  the  hand).    

-­‐ Hyperextensibility.    

• Toxic  shock  syndrome  (TSS)    

-­‐ Potentially  fatal  illness  caused  by  a  bacterial  toxin.  

-­‐ Staphylococcus  aureus  and  Streptococcus  pyogenes.  

-­‐ Diffuse   rash,   intense   erythroderma,   blanching   with   subsequent  desquamation,  especially  of  the  palms  and  soles.  

-­‐ Tampons  and  septicemia.    

 

   

• Tylosis  –  Rare  inherited  disease  characterized  by  excess  skin  on   the   palms   and   soles.   Affected   patients   have   a   much   higher   probability   of   developing   esophageal   cancer   than   the   general   population.      

 

• Nail-­‐pitting  –  Psoriasis.    

• Beau’s  lines  –  Unwell.    

• Koilonychia  –  Iron  deficiency.  

• Pigmentation   of   nails   –   Zidovudine.   Bluish   or   brownish-­‐black   discoloration  of  nails  may  develop  during  the  first  month  or  two   of  zidovudine  therapy  and  usually  disappears  within  2  months  if   the  drug  is  discontinued.  Discoloration  may  occur  as  longitudinal   streaks  or  transverse  bands.  

 

• Charcot  Marie  Tooth  

-­‐ An   inherited   disorder   of   nerves   (neuropathy)   that   takes   different  forms.  

-­‐ Characterized   by   loss   of   muscle   tissue   and   touch   sensation,   predominantly  in  the  feet  and  legs  but  also  in  the  hands  and   arms  in  the  advanced  stages  of  disease.    

-­‐ Usually,  the  initial  symptom  is  foot  drop  early  in  the  course   of  the  disease.  This  can  also  cause  claw  toe,  where  the  toes   are   always   curled.   Wasting   of   muscle   tissue   of   the   lower   parts   of   the   legs   may   give   rise   to   "stork   leg"   or   "inverted   bottle"   appearance.   Weakness   in   the   hands   and   forearms   occurs  in  many  people  later  in  life  as  the  disease  progresses.  

-­‐ Breathing   can   be   affected   in   some;   so   can   hearing,   vision,   and  the  neck  and  shoulder  muscles.  Scoliosis  is  common.  Hip   sockets  can  be  malformed.  Gastrointestinal  problems  can  be   part  of  CMT,  as  can  chewing,  swallowing,  and  speaking  (vocal   cords  atrophy).  A  tremor  can  develop  as  muscles  waste.    

Clubbing  

  • Endocarditis.  

• Congenital  cyanotic  heart  disease.    

• PDA  complicated  by  Eisenmenger  (only  toes,  distal  to  SCA).    

• Bronchiectasis.  

• Lung  abscess.  

• CA  lung.  

• Idiopathic  lung  disease.  

• IBD.  

• Liver  disease.  

• Thyrotoxicosis.  

• Atrial  myxoma  

• Fibrous  alveolitis.  

*  NOT  in  COPD.    

Thenar   muscles  

Flattened  –  Median  nerve  palsy.    

• Bilateral  carpal  tunnel  

• Acromealgy  

Chronic,  slowly  progressing,  highly  variable  inherited  multi-­‐systemic   disease.  

• Stiff  handshake,  cannot  let  go.    

• Sad,  shabby,  droopy  face.    

• Wasting  of  the  face  (triangular  face,  lower  half  of  face  sunken).  

• Marked  wasting  of  the  neck  muscles  –  May  have  floppy  neck.    

• Bilateral  ptosis.    

 

    Rheumatoid   arthritis    

   

• Swan   neck   deformity   –   DIP   hyperflexion   with   PIP   hyperextension.    

• Boutonniere's  deformity    

• Z   deformity   of   thumb   –   Hyperextension   of   the   interphalangeal   joint,   and   fixed   flexion   and   subluxation   of   the   metacarpophalangeal  joint.  

• Finger  ulnar  deviation  (MCP).    

Hepatology  

and  nails   • Palmar  erythema  –  Liver  failure,  PRV,  pregnancy,  thyrotoxicosis.    

• Terry’s   nail   (leukonychia,   white   nails)   –   Hypoalbuminaemia   caused  by  nephrotic  syndrome.    

• Half  and  half  nails  ("Lindsay's  nails")  

-­‐ Proximal   portion   of   the   nail   white   and   the   distal   half   red,   pink,  or  brown,  with  a  sharp  line  of  demarcation  between  the   two  halves.  

-­‐ Chronic  renal  failure.    

• Ehlers–Danlos  syndrome  (EDS)  

-­‐ A   group   of   more   than   10   different   inherited   disorders;   all   involve   a   genetic   defect   in   collagen   and   connective-­‐tissue   synthesis  and  structure.  

-­‐ Can  affect  the  skin,  joints,  and  blood  vessels.    

 

Scarlet  fever  

• Caused  by  exotoxin  released  by  Streptococcus  pyogenes.  

• Characterized  by   (1) Sore  throat.  

(2) Fever.  

(3) Bright   red   tongue   with   a   “strawberry”   appearance   –   Inflamed   red   papillae.  

Seen  in  Kawasaki  disease,  toxic  shock  syndrome,  and  scarlet  fever.  May  mimic   glossitis  or  B12  vitamin  deficiency.    

*   Kawasaki   disease   –   An   autoimmune   disease   that   manifests   as   a   systemic   necrotizing  medium-­‐sized  vessel  vasculitis  and  is  largely  seen  in  children  less  than   5  years  of  age.  It  affects  many  organ  systems,  mainly  those  including  the  blood   vessels,   skin,   mucous   membranes   and   lymph   nodes;   however,   its   most   serious  

(4) Characteristic  rash.    

-­‐ Fine,  red,  and  rough-­‐textured.  Blanches  upon  pressure.  

-­‐ Generally  starts  on  the  chest,  armpits,  and  behind  the  ears.  

-­‐ Spares  the  face  (although  some  circumoral  pallor  is  characteristic).  

-­‐ Worse   in   the   skin   folds.   These   Pastia   lines   (where   the   rash   runs   together   in   the  armpits  and  groin)  appear  and  can  persist  after  the  rash  is  gone.  

-­‐ May  spread  to  cover  the  uvula.  

 

Reddened  sore  throat,  a  fever  at  or  above  101  °F  (38.3  °C),  and  swollen  glands  in  the   neck.  The  tonsils  and  back  of  the  throat  may  be  covered  with  a  whitish  coating,  or   appear  red,  swollen,  and  dotted  with  whitish  or  yellowish  specks  of  pus.  Early  in  the   infection,   the   tongue   may   have   a   whitish   or   yellowish   coating.   Also,   an   infected   person  may  have  chills,  body  aches,  nausea,  vomiting,  and  loss  of  appetite.  

       

Hansen’s  disease/Leprosy    

• Chronic   disease   caused   by   the   bacteria   Mycobacterium   leprae   and   Mycobacterium  lepromatosis.  

• Primarily   a   granulomatous   disease   of   the   peripheral   nerves   and   mucosa   of   the   upper  respiratory  tract;  skin  lesions  are  the  primary  external  sign.  

• Left   untreated,   leprosy   can   be   progressive,   causing   permanent   damage   to   the   skin,  nerves,  limbs  and  eyes.  Contrary  to  folklore,  leprosy  does  not  cause  body   parts   to   fall   off,   although   they   can   become   numb   or   diseased   as   a   result   of   infection;  infection  results  in  tissue  loss,  so  fingers  and  toes  become  shortened   and  deformed  as  the  cartilage  is  absorbed  into  the  body.  

   

69)  On  DOPES!  

Dear  Yin  Ling,  

We  must  not  allow  Dopeys  in  medicine!  That  is  only  allowed  in  the  7  dwarfs!  

No  apex  beat  felt  -­‐  WHY?  

Remember  DOPES    

Dextrocardia  (pls  don't  say  this  first!),   Obesity,  

Pleural/Pericardial  effusion,   Emphysema,  Empyema   Shock,  Silly  medical  student    

 

70)  on  Eating  

Yin  ling  says  I  feed  her  too  much  at  dinner  and  hence  she  is  sleepy  post  dinner!  True   or  false?  

Is  there  a  physiological  basis?    

Did  your  teachers  in  year  1  teach  you  well?    

   

High-­‐carb,  high-­‐fat  foods  (like  most  Msian  meals  esp  my  beloved  Hokkien  mee)   trigger  a  neural  response  when  it  reaches  the  small  intestine.  Thats  why  your   sleepiness  is  Not  instant  but  after  an  hour  or  so.    

That  response,  via  the  parasympathetic  nervous  system,  focus  on  moving  the   intestines  and  digesting  the  food  rather  than  study.  Think  of  the  python  after  

swallowing  a  chicken...  it  lies  flat  and  unmoving  like  my  med  students!    

 

A  group  of  brain  cells  called  orexin  neurons  are  found  in  the  hypothalmus  and  are   very  sensitive  to  glucose  levels,  which  spike  after  a  CHO  meal.  These  neurons   produce  orexin,  which  moderates  wakefulness  in  the  brain.  

 

But  orexin  isn't  the  only  sleep-­‐related  neurohormone  affected  by  food.  As  the   quantity  of  food  increases,  so  too  is  the  amount  of  insulin  released.  The  insulin   increases  the  amount  of  seratonin  and  melatonin  that  flood  the  brain,  two  

chemicals  associated  with  drowsiness  (and,  for  that  matter,  happiness).  Remember   the  Melatonin  tablet  sold  at  airports  to  help  travellers  sleep?  Now  you  know  also   why  when  some  people  are  stressed  they  EAT!  Natural  SSRI  !  

 

Hence  we  feel  Happy  after  our  CNY  reunion  dinner.  Drinking  tea  helps  to  keep  us   awake.  And  we  just  want  to  slouch  on  the  sofa  and  sing  or  chit  chat  or  'chill'      

So  what  can  the  med  student  or  post  grad  do  to  solve  this  dilemma?  Easy.  Give  me   the  food.  I  can  afford  to  sleep!  

   

71)  on  Beta  blockers  and  Hypoglycaemia    

Dear  Yin  Ling,  

What  hypoglycemic  symptom  is  not  masked  by  beta  blockers?  

 

Symptoms  and  Signs  of  Hypoglycemia   Autonomic:     Loss  of  concentration     Drowsiness    

Dizziness     Hemiplegia    

Arrhythmias,  Seizures,  Coma,  Death  

In document Historia de Nuestra Señora de la Balma (página 131-138)